Chest wall reconstruction in Poland Syndrome: An analysis of surgical techniques and clinical manifestations

Authors

  • Pedro Fechine Honorato
  • Anna Vitória Paz Moreira
  • Dhiego Alves de Lacerda
  • Isabelle Lima Lustosa
  • Renata Silva Cezar
  • Arthur de Sousa Lima Carvalho
  • Jalles Dantas de Lucena

Keywords:

Anatomy, Surgery, Poland Syndrome.

Abstract

Poland Syndrome, a rare congenital malformation identified in 1841, is characterized by the absence of the sternocostal portion of the pectoralis major muscle, usually unilaterally, accompanied by symptoms such as thoracic asymmetry and breast hypotrophy. In severe forms, bone and kidney changes can occur. The condition, with a variable incidence of between 1:7,000 and 1:100,000 live births, has a multifactorial etiology involving genetic and environmental factors. Diagnosis, often underdiagnosed due to its aesthetic focus, is usually clinical, with confirmation by imaging tests and aspiration cytology. Various surgical techniques, such as myocutaneous flaps and silicone implants, are used for correction, adapting to the patient's needs. This study aims to describe the main clinical findings and surgical techniques available to correct Poland's Syndrome.

DOI: 10.56238/sevenVmulti2024-180

Published

2024-04-18