Anthrophophysiological analysis in a patient with Progressive Ossificant Fibrodysplasia: Casuistic

Abstract

The objective was to measure anthropophysiological variables in patients with FOP, comparing them to standards. For this, ECG / ECC, tomography, pulmonary functions, manovacuometry, bioimpedance, blood analysis and goniometry were performed. The resultsAA = 27 mm; LA = 26 mm; LV = 41 mm; RV = 30 mm; FSD-LV = 20 mm; septum = 5 mm; LV-BWLV = 5 mm; LA/AA = 0.96, FE = 83%; septum/BWLV = 1.00, FDV = 74 ml; SV = 61 ml; volume/mass = 1.03 ml / g; Normalized GSF-LV; under bronchodilator, FVC, FEV1 and PEF = 54%, 64% and 81% of the predictors; FEV1% and 2575 = 118% and 116% of the predictors; MEP = 65 mmH (↓42.7%) and MIP = 55 mmHg (↓63.2%); BM = 39.0 kg; h = 1.57 m; BMI = 15.8 k/m2; AC = 64 cm; % FM = 26%; MM = 27.39 kg; BMC = 1.53 kg; FLM = 28.92 kg; RIMM = 4.5 kg / m2; OI = 63.50%; normal blood glucose, triglycerides and CRP; RS, LS, LH, RA and LA = 0º, LK = 25º, RK = 40º, LE = 55º, RH = 110º, RE = 150º. The cardiovascular differences did not cause any dysfunction. FOP caused moderate restrictive respiratory disorder, Pimax / Pmax below the predictors, MC, h, BMI, CA, bone mineral content, low MLG and IO, immobility in 05 joints and impairment in 03, with 02 preserved. It was concluded that FOP is significantly compromising the respiratory system, with moderate restrictive respiratory disorder caused by the sharp convexity thoracic scoliosis directed to the left, due to the compromised position of bipedation due to the new calcifications, in addition to compromised movement and walking.

DOI:https://doi.org/10.56238/uniknowindevolp-032