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Castleman's syndrome: Main sonographic findings

Bitencourt CAR;
Pereira LR;
Azeredo LM;
Ayub ES;
Silva CHM;
Silva TF;
Flister DPV;
Motta LTS;
Lancuna HC

Cecília de Almeida Ruas Bitencourt

Leonardo Robleto Pereira

Letícia Martins Azeredo

Elizabeth Sanchez Ayub

Carlos Henrique Mascarenhas Silva

Tiago Ferreira Silva

Darlyane Paula Vieira Flister

Luiza Teixeira Sarah Motta

Henrique Cezar Lancuna


Keywords

Castleman's disease
Castleman's tumor
Lymphoproliferative disorders
Lymphadenopathy
Radiology
Diagnostic imaging
Doppler ultrasonography of vessels

Abstract

Castleman's disease is a rare, usually benign, lymph node disorder that can manifest as cervical or mediastinal adenopathy. There are three histological variants: unicentric hyaline-vascular, unicentric plasma cells, and multicentric plasma cells, each with different symptoms and radiological features. The hyaline vascular form has a predilection for the thorax, and can simulate other conditions such as thymoma or lymphoma. Imaging tests, such as CT scans and MRIs, are useful for diagnosis, revealing characteristic patterns of lymph node enhancement and involvement. Treatment varies depending on the variant of the disease and may include surgery, steroids, chemotherapy, or antiviral therapy. Accurate diagnosis is challenging, requiring attention from radiologists to differentiate Castleman's disease from other lymphoproliferative conditions. This report aims to describe the clinical case of a patient admitted to the emergency department with pain in the left hypochondrium and to warn about the need for early diagnosis and follow-up for appropriate therapy.

 

DOI:https://doi.org/10.56238/interdiinovationscrese-043


Creative Commons License

This work is licensed under a Creative Commons Attribution-NonCommercial 4.0 International License.

Copyright (c) 2023 Carlos André Tavares de Moura, Fernando B. Mainier , Paulo Roberto Duailibe Monteiro

Author(s)

  • Cecília de Almeida Ruas Bitencourt
  • Leonardo Robleto Pereira
  • Letícia Martins Azeredo
  • Elizabeth Sanchez Ayub
  • Carlos Henrique Mascarenhas Silva
  • Tiago Ferreira Silva
  • Darlyane Paula Vieira Flister
  • Luiza Teixeira Sarah Motta
  • Henrique Cezar Lancuna